امفالوسل و قلب بیرون از قفسه سینه درنوزاد با Pentalogy of Cantrell
Authors
Abstract:
Background : Pentalogy of Cantrell is a very rare congenital anomaly which is diagnosed with severe thoracoabdominal defect, omphalocele, lower sternal defect, anterior diaphragmatic defect anterior pericardial defect and ectopia cordis.Pathogenesis is unknown, mesodermal developmental defects in 14-18 days after conception maybe responsible . Case Report: The case is newborn with omphalocele and ectopia cordis. Conclusion: All newborns with omphalocele must be evaluated for Pentalogy of Cantrell and accompanying anomaly.
similar resources
امفالوسل و قلب بیرون از قفسه سینه درنوزاد با pentalogy of cantrell
بحث و نتیجه گیری: در تمام موارد ابتلا به امفالوسل بررسی از نظر وجود پنتالوژی کانترل و آنومالی همراه توصیه می شود. معرفی مورد: در این مقاله نوزاد مبتلا به امفالوسل و قلب بیرون از قفسه سینه (ectopia cordis) معرفی می شود . مقدمه: پنتالوژی کانترلpentalogy of cantrell) ) اختلال مادرزادی بسیار نادری است که با نواقص شدید قفسه سینه و شکم شامل بیرون زدگی احشاء از محل بندناف (امفالوسل)، نقص قسمت پایینی ج...
full textPentalogy of Cantrell Cantrell pentalojisi
Ectopia cordis is a rare malformation presenting as an isolated lesion or as part of the Cantrell’s pentalogy syndrome characterized by midline closure defects. A preterm male baby who did not have antenatal follow-up was born by caesarean section with evisceration of the heart and major parts of the intraabdominal organs. Combination of these findings suggested the diagnosis of Cantrell’s pent...
full textPentalogy of Cantrell
Özet İlk olarak 1958 yılında Cantrell, Haller ve Ravitch tarafından tanımlanan Cantrell sendromu, ektopia kordis ile birlikte diyafragma, orta hat karın duvarı ve perikardı etkileyen nadir görülen bir anomalidir. Cantrell sendromu sıklıkla intrakardiyak defektler ile birliktelik göstermektedir. Kompleks kardiyak anomali prognozu belirlemede önemli bir role sahiptir. Çeşitli derecelerde birçok s...
full textAn incomplete pentalogy of Cantrell.
Pentalogy of Cantrell is a rare entity of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium and heart. The complete pentalogy and its variants have been described in the literature. We report a 47-day-old girl with an incomplete pentalogy of Cantrell presenting with congenital absence of the sternum, congenital heart defects, and an epigastric hernia. Two even rar...
full textPentalogy of Cantrell: the complete spectrum.
To cite: Martins CF, Serras I, Santos AV, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2014-207556 DESCRIPTION A healthy 25-year-old primigravida, without a history of teratogenic exposition, presented to our hospital with a first trimester routine ultrasonographic examination showing two major fetal defects: gastrosquisis (figure 1 and video 1) and ect...
full textPentalogy of Cantrell: a case report
Cantrell's pentalogy (CP), a rare congenital malformation, consists of the supraumbilical abdominal wall defect, the sterna lower part defect and agenesis of the anterior portion of the diaphragm, an absence of the diaphragmatic part of the pericardium, and a malformation of cardia. This case report presents a female neonate, who was born at 32 weeks of conception, weighing 1300 g and was admit...
full textMy Resources
Journal title
volume 14 issue None
pages 113- 117
publication date 2012-09
By following a journal you will be notified via email when a new issue of this journal is published.
No Keywords
Hosted on Doprax cloud platform doprax.com
copyright © 2015-2023